Patient Subgroup

Decision to Treat

Asymptomatic Patients

No Treatment

Mild Pulmonary dysfunction, minimal functional limitation

Observation, no treatment

Patients with excellent prognosis (eg. erythema nodosum)

Observation, attempt palliative therapy (see text)

Mild to moderate pulmonary dysfunction, mild to moderate functional limitation

Treatment vs. observation for deterioration. If observed, treat if deterioration occurs. Consider treatment if no improvement after 3 - 6 months

Severe pulmonary dysfunction, severe functional limitation

Treatment